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Kasai-Like Repair of Distant and Recurrent Pulmonary Venous Obstruction After Repair of Total Anomalous Pulmonary Venous Return

Presented By:

Majid Husain, Thayne Dalrymple, Megan Schultz, Ashley Prosper, Daniel Levi, Glen Van Arsdell

University of California, Los Angeles (UCLA)

MajidHusain@mednet.ucla.edu

Overview:

Pulmonary venous obstruction (PVO) remains a major complication and the main cause of reoperation following repair of total anomalous pulmonary venous return (TAPVR). While a primary sutureless repair is preferred to address this pathology, employment of such a technique can be limited by distant PVO. We describe a repair to address hilar pulmonary vein obstruction in two patients with infradiaphragmatic TAPVR in whom a standard sutureless repair was not feasible. The repair is analogous to the Kasai repair for biliary atresia and involves a lung hilum Kasai-type anastomosis of either the atrium or conduit to address these challenges and add to the repertoire of the surgeon.